Pulmonic Valve Disorders & Pulmonary Valve Disease

Overview

What are pulmonic valve disorders and pulmonary valve disease?

Pulmonic valve disorders refer to problems with the pulmonic valve, which is one of the four valves in your heart. This valve sits between the right ventricle (one of the heart’s lower chambers) and the pulmonary artery, which carries blood to the lungs. The main job of the pulmonic valve is to help blood flow smoothly from the heart to the lungs, where it picks up oxygen. When this valve doesn't work properly, it can cause blood flow problems that may affect your heart and lungs. There are different types of pulmonic valve disorders, including:

  • Pulmonic stenosis: This occurs when the valve is too narrow, making it harder for blood to flow from the heart to the lungs.
  • Pulmonic regurgitation: This happens when the valve does not close properly, allowing blood to leak back into the heart from the pulmonary artery.
  • Pulmonic atresia: A more severe form present from birth, where the valve is missing or underdeveloped, preventing normal blood flow from the heart to the lungs. 

What are pulmonic valve disorder symptoms?

Pulmonic valve disorders can cause a range of symptoms, depending on the severity of the condition. Some people may have no symptoms, especially in mild cases. When symptoms do occur, they can include:

  • Shortness of breath: Difficulty breathing, especially during exercise or physical activity.
  • Fatigue: Feeling unusually tired or weak, even with normal activities.
  • Chest pain or discomfort: A feeling of pressure or pain in the chest.
  • Heart palpitations: Feeling like your heart is racing, pounding or skipping beats.
  • Swelling in the legs or abdomen: Caused by fluid buildup due to poor blood flow.
  • Fainting or dizziness: Often related to reduced blood flow to the brain.

What causes pulmonic valve disorders?

Pulmonic valve disorders can develop for various reasons, including: 

  • Congenital heart defects: Some people are born with pulmonic valve problems, such as pulmonic stenosis or atresia, which are present from birth.
  • Rheumatic fever: A complication of untreated strep throat that can damage the heart valves, including the pulmonic valve.
  • Infective endocarditis: A bacterial infection that affects the heart valves, causing them to become damaged or leaky.
  • Carcinoid syndrome: A rare condition where cancerous tumors produce substances that can damage the heart valves, including the pulmonic valve.
  • Pulmonary hypertension: High blood pressure in the arteries of the lungs can cause the pulmonic valve to leak or malfunction. 

How doctors diagnose pulmonic valve disorders

Diagnosing pulmonic valve disorders usually involves a combination of a physical exam, listening to the heart and imaging tests to see how well the valve is working. Common diagnostic methods include:

  • Physical exam and listening to the heart: Doctors can often detect abnormal heart sounds, such as a murmur, which may suggest a valve problem.
  • Echocardiogram (Echo): This is the main test used to diagnose valve disorders. It uses sound waves to create detailed images of the heart, showing how the valves and chambers are functioning.
  • Electrocardiogram (EKG/ECG): This test records the electrical activity of the heart and can help detect rhythm problems or other signs of heart strain.
  • Cardiac MRI or CT scan: Advanced imaging tests that provide a detailed look at the heart and valves.
  • Cardiac catheterization: A more invasive test where a thin tube (catheter) is inserted into a blood vessel and guided to the heart to measure pressures and evaluate the valve. 

How to treat pulmonic valve disorders

Treatment for pulmonic valve disorders depends on the type and severity of the condition. Options range from monitoring to medications or surgical procedures. Mild cases without symptoms may only need regular check-ups and echocardiograms to monitor the condition.

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Medication

Medications may be prescribed to manage symptoms, reduce fluid buildup or treat underlying conditions like high blood pressure.

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Procedures or surgery

  • Balloon valvuloplasty: For pulmonic stenosis, a procedure called balloon valvuloplasty may be used. A balloon is inserted via a catheter and inflated to widen the narrowed valve.
  • Valve repair or replacement surgery: In more severe cases, surgery may be needed to repair the valve or replace it with a new one, which can be a mechanical valve or one made from animal tissue.
  • Transcatheter pulmonary valve replacement (TPVR): A minimally invasive procedure where a new valve is delivered via a catheter, without open-heart surgery.

How to prevent pulmonic valve disorders

While some pulmonic valve disorders, particularly congenital ones, cannot be prevented, there are steps you can take to reduce your risk of developing valve problems later in life:

  • Treat infections promptly: Properly treating strep throat can prevent rheumatic fever, which can damage heart valves.
  • Good dental hygiene: Regular dental care and good oral hygiene can reduce the risk of infective endocarditis, which can affect the heart valves.
  • Healthy lifestyle: Managing risk factors such as high blood pressure, avoiding smoking, eating a healthy diet and exercising regularly can help keep your heart and valves healthy.
  • Regular check-ups: If you have risk factors for heart valve disease, regular medical check-ups can help detect problems early.

Outlook

The outlook for pulmonic valve disorders varies depending on the severity of the condition and the type of treatment received. Many people with mild conditions can live normal, healthy lives with regular monitoring. For those who need treatment, the success rate of procedures like valve repair or replacement is generally high and they can greatly improve symptoms and quality of life. However, ongoing follow-up care is essential to monitor the heart’s function and ensure the valve is working properly.

Pulmonic valve disorder treatment near you

Cardiology services at Ballad Health

Our extensive network of highly trained cardiologists, surgeons and advanced practice providers are here to support you and help you navigate a heart-related diagnosis.

Learn more about heart and vascular services at Ballad Health.

CVA Heart Institute Learning Center

We understand that receiving a pulmonic valve disorder diagnosis can be overwhelming. Our goal is to alleviate your fears and help you to understand your condition. 

We have an informational video library, education tools and heart-related FAQs so that you have the resources you need.

Heart care patient stories

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Tony Buchanan cardiac patient
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Shelia sitting on a park bench, reading a book on a beautiful sunny day
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Read our patient stories

Our patients inspire us every day, and we’re honored when they trust us with their care. They tell their stories best, so we’ve gathered a few here to share with you.

Many of these patients received life-saving care for heart conditions when they weren’t experiencing any symptoms. These experiences have changed they way they look at their individual care and helped them see the importance of regular preventive screenings.